Intrathoracic ectopic kidney is a very rare form of ectopic kidney.It is usually asymptomatic and diagnosed incidentally during chest investigations.A 3-year-old boy was admitted Bento Box to our center with respiratory distress and fever recurrent since birth.
An abdominal ultrasound, chest X-ray, intravenous pyelogram, and computed tomography revealed a right-sided intrathoracic ectopic kidney.A thoracotomy approach was used.The right intrathoracic ectopic kidney was reduced to the abdominal cavity and a diaphragm fold was performed.
Subsequently, severe hydronephrosis and obstruction as headlight a result of ureteral folding required repeated surgical intervention.